Surgery for secondary pneumothorax caused by Hermansky–Pudlak syndrome
نویسندگان
چکیده
منابع مشابه
Surgery for secondary pneumothorax caused by Hermansky-Pudlak syndrome.
In this large population based study, we found that people with IPF have higher incidence rates of pulmonary embolus and DVT, and are more likely to be prescribed warfarin, compared with the general population. Possible explanations for our finding include 1) IPF increasing the risk of VTE, and 2) a prothrombotic state leading to the development of IPF and VTE. This study supports the hypothesi...
متن کاملSurgery for secondary pneumothorax caused by Hermansky–Pudlak syndrome
Hermansky–Pudlak syndrome (HPS) is a rare, heterogeneously inherited, autosomal recessive group of disorders presenting with a triad of oculocutaneous albinism, a haemorrhagic defect secondary to platelet dysfunction and accumulation of ceroid-like material in the reticuloendothelial system [1, 2]. Although pulmonary fibrosis has occurred in a number of patients with this syndrome and generally...
متن کاملOutcome of Video-assisted Thoracoscopic Surgery for Spontaneous Secondary Pneumothorax
BACKGROUND Conventional treatment (i.e. chest tube insertion and chemical pleurodesis) still remains standard for patients with secondary spontaneous pneumothorax because the risk of surgical bullectomy is deemed high in this subset. However, it has been suggested that surgical treatment using thoracoscopy may expedite postoperative recovery and, thus, may reduce hospital stay. MATERIALS AND ...
متن کاملRecurrent catamenial pneumothorax caused by diaphragmatic fenestration.
Catamenial pneumothorax, which is a rare cause of spontaneous pneumothorax, is defined as a pneumothorax that starts at the onset of or within the first 72 hours of the menstruation period in women.1 Catamenial pneumothorax was first described by Maurer et al in 1958.2 The reported incidence of catamenial pneumothorax among the spontaneous pneumothoraces is 3–6%, but the actual incidence is 25–...
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Background Thoracic endometriosis syndrome is a rare form of extrapelvic endometriosis characterized by the presence of functioning endometrial tissue in pleura, lung parenchyma, and airways, associated with a high rate of infertility. Case Report We have reported a case of successful management and treatment of thoracic endometriosis syndrome that occurred in a 37-year-old female patient. Sh...
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ژورنال
عنوان ژورنال: European Respiratory Journal
سال: 2014
ISSN: 0903-1936,1399-3003
DOI: 10.1183/09031936.00107714